Primary Small Bowel Neurofibroma Induced Intussusception Complicated with Small Bowel Obstruction and Perforation: A Case Report

Muhamad Zabidi Ahmad

Abstract


Neurofibromatosis (NF) is a genetic neurological disorder which can lead to abnormal tumour suppression. Neurofibromatosis associated neurological tumour is usually benign in nature, only occasionally can become malignant. Gastrointestinal involvement is reported to be infrequent with only up to 25% of patients with neurofibromatosis showing involvement. Solitary gastrointestinal neurofibroma is very rare, with most cases involving the stomach or small bowel. We report here a case of solitary small intestinal neurofibroma with no other associated systemic signs, causing intussusception and intestinal obstruction.


Keywords


Neurofibromatosis, gastrointestinal neurofibroma, intussusception, intestinal obstruction, small intestine

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